Portal Cavernoma Cholangiopathy Due To Extrahepatic Portal Vein and Supra-Mesenteric Vein Thromboses Associated with Congenital Protein C Deficiency in a Young Adult
نویسندگان
چکیده
منابع مشابه
Extrahepatic Portal Vein Aneurysm
Portal vein aneurysms are rare vascular abnormalities, many of which are incidentally discovered on routine imaging studies. The etiology of portal venous aneurysms is poorly understood, and the management of these lesions is debatable. We report the case of a 61-year-old woman with extrahepatic portal vein aneurysm. We review the nature and significance of this abnormality and discuss appropri...
متن کاملTherapeutic Challenges for Symptomatic Portal Cavernoma Cholangiopathy.
Although transjugular intrahepatic portosystemic shunts are most frequently used for the management of portal hypertension, the surgical approach is preferred for symptomatic portal cavernoma cholangiopathy. We present the case of a 25-year old female patient with a portal cavernoma secondary to catheterization of the umbilical vein at birth. She had had two episodes of esophageal variceal blee...
متن کاملExtrahepatic portal hypertension due to familial protein S deficiency.
Portal vein thrombosis (PVT) is a common cause of portal hypertension in children. A majority of children with PVT of unknown etiology have functional Protein C deficiency or abnormally elevated levels of anti-cardiolipin antibodies. We report an 8 years old Indian girl with portal cavernoma due to hereditary Protein S deficiency. We documented familial deficiency of Protein S in 2 asymptomatic...
متن کاملPortal vein and superior mesenteric vein thrombosis after cesarean hysterectomy
1. Chawla Y, Duseja A, Dhiman RK. Review article: The modern management of portal vein thrombosis. Aliment Pharmacol Ther 2009;30:881-94. 2. Ponziani FR, Zocco MA, Campanale C, Rinninella E, Tortora A, Maurizio L, et al. Portal vein thrombosis: Insight into physiopathology, diagnosis and treatment. World J Gastroenterol 2010; 16:143-55. 3. Distefano G, Rodono A, Cilauro S, Saporito A, Pennisi F...
متن کاملCongenital abnormalities associated with extrahepatic portal hypertension.
Congenital abnormalities were present in 12 out of 30 (40%) children with extrahepatic portal hypertension of unknown cause, but in only 2 out of 17 (12%) children with extnahepatic portal hypertension secondary to umbilical vein catheterization or omphalitis. The most frequent abnormalities in this series and in published reports were atrial septal defect, malformation of the biliary tract, an...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Archives of Clinical and Medical Case Reports
سال: 2019
ISSN: 2575-9655
DOI: 10.26502/acmcr.96550117